Marfan syndrome (MFS) is an autosomal dominant hereditary condition. Individuals with MFS face an increased risk of aortic dissection, and pregnancy itself is also recognized as a period of heightened risk for this complication. In pregnant women with Marfan syndrome, an elevated risk for aortic dissection is described as well as more adverse fetal outcomes compared to pregnant women without MFS. This emphasizes the need and importance for careful management, which will be researched in this paper.